branched chain aminotransferase 2, mitochondrial
| GO Term | Evidence Code | PMID |
|---|---|---|
| isoleucine metabolic process | ||
| isoleucine catabolic process | ||
| isoleucine catabolic process | ||
| leucine metabolic process | ||
| valine metabolic process |
| GO Term | Evidence Code | PMID |
|---|---|---|
| nucleoplasm | ||
| nucleoplasm | ||
| mitochondrion | ||
| mitochondrion | ||
| mitochondrion |
| GO Term | Evidence Code | PMID |
|---|---|---|
| branched-chain-amino-acid transaminase activity | ||
| branched-chain-amino-acid transaminase activity | ||
| branched-chain-amino-acid transaminase activity | ||
| L-leucine transaminase activity | ||
| L-leucine transaminase activity |
| DO ID | Disease Name | Source |
|---|---|---|
| DOID:9269 | maple syrup urine disease |
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Supported by JST NBDC Grant Number JPMJND2204
Partly supported by NIH Common Fund Grant #1U01GM125267-01
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Last updated: December 8, 2025