Cystic fibrosis transmembrane conductance regulator

Summary
UniProt ID
P26362
Gene Symbol
  • ABCC7
  • CFTR
  • DFTR
Organism
Squalus acanthias (spiny dogfish)
PubChem
P26362
Re-Glyco
P26362
Annotation
Keyword
  • ATP-binding
  • Cell membrane
  • Chloride channel
  • Endoplasmic reticulum
  • Endosome
  • Glycoprotein
  • Isomerase
  • Phosphoprotein
  • Repeat
  • Transmembrane helix
Gene Ontology (GO)
Sequence
MQRSPIEKANAFSKLFFRWPRPILKKGYRQKLELSDIYQIPSSDSADELSEMLEREWDRELATSKKNPKLVNALRRCFFWRFLFYGILLYFVEFTKAVQPLCLGRIIASYNAKNTYEREIAYYLALGLCLLFVVRTLFLHPAVFGLQHLGMQMRIALFSLIYKKILKMSSRVLDKIDTGQLVSLLSNNLNKFDEGVAVAHFVWIAPVQVVLLMGLIWNELTEFVFCGLGFLIMLALFQAWLGKKMMQYRDKRAGKINERLAITSEIIDNIQSVKVYCWEDAMEKIIDDIRQVELKLTRKVAYCRYFSSSAFFFSGFFVVFLSVVPYAFIHTIKLRRIFTTISYNIVLRMTVTRQFPSAIQTWYDSLGAIRKIQDFLHKDEHKTVEYNLTTKEVEMVNVTASWDEGIGELFEKVKQNDSERKMANGDDGLFFSNFSLHVTPVLKNISFKLEKGELLAIAGSTGSGKSSLLMMIMGELEPSDGKIKHSGRISYSPQVPWIMPGTIKDNIIFGLSYDEYRYTSVVNACQLEEDITVFPNKDKTVLGDGGITLSGGQRARISLARALYKDADLYLLDSPFSHLDVTTEKDIFESCLCKLMVNKTRILVTSKLEHLKKADKILLLHEGHCYFYGTFSELQGEKPDFSSQLLGSVHFDSFSAERRNSILTETFRRCSVSSGDGAGLGSYSETRKASFKQPPPEFNEKRKSSLIVNPITSNKKFSLVQTAMSYPQTNGMEDATSEPGERHFSLIPENELGEPTKPRSNIFKSELPFQAHRRQSVLALMTHSSTSPNKIHARRSAVRKMSMLSQTNFASSEIDIYSRRLSEDGSFEISEEINEEDLKECFADEEEIQNVTTTWSTYLRYVTTNRNLVFVLILCLVIFLAEVAASLAGLWIISGLAINTGSQTNDTSTDLSHLSVFSKFITNGSHYYIFYIYVGLADSFLALGVIRGLPLVHTLVTVSKDLHKQMLHSVLQGPMTAFNKMKAGRILNRFIKDTAIIDDMLPLTVFDFVQLILIVVGAICVVSVLQPYTLLAAIPVAVIFIMLRAYFLRTSQQLKQLESEARSPIFSHLITSLRGLWTVRAFGRQSYFETLFHKALNLHTANWFLYLSTLRWFQMRIDIVFVLFFIAVTFIAIATHDVGEGQVGIILTLAMNITSTLQWAVNSSIDVDGLMRSVSRVFKYIDIPPEGSETKNRHNANNPSDVLVIENKHLTKEWPSGGQMMVNNLTAKYTSDGRAVLQDLSFSVNAGQRVGLLGRTGAGKSTLLSALLRLLSTEGEIQIDGISWNSVSLQKWRKAFGVIPQKVFVFSGTFRKNLDPYEQWSDEEIWKVTEEVGLKSMIEQFPDKLNFVLVDGGYILSNGHKQLMCLARSILSKAKILLLDEPTAHLDPVTFQIIRKTLKHTFSNCTVILSEHRVEALLECQQFLVIEGCSVKQFDALQKLLTEASLFKQVFGHLDRAKLFTAHRRNSSKRKTRPKISALQEEAEEDLQETRL
Glycosylation Sites
Displaying all 2 entries
Position Description PubMed ID GlyTouCan ID Source
905 N-linked (GlcNAc...) asparagine
923 N-linked (GlcNAc...) asparagine
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt

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Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 6, 2026