IgA vasculitis

Summary
Synonym
  • Allergic purpura
  • Autoimmune purpura
  • HSP
  • Henoch Schoenlein purpura
  • Henoch Scholein purpura
  • Henoch Schonlein purpura
  • Henoch Schönlein purpura
  • Henoch-Schoenlein purpura
  • Henoch-Scholein purpura
  • Henoch-Schonlein purpura
  • Henoch-Schönlein purpura
  • IgAV
  • Purpura, autoimmune
  • immunoglobulin A vasculitis
Definition
A hypersensitivity vasculitis that is characterized by purpura (purplish plaques), arthralgia, gastrointestinal upset, and/or glomerulonephritis, and may be related to increased immune response following an infection.
Super Class
hypersensitivity vasculitis
Disease Ontology
DOID:11123
Mondo Disease Ontology
MeSH
UMLS
NCI Thesaurus
ORDO
GARD
Related Genes
Displaying all 8 entries
Gene ID Gene Symbol Description Source
183 AGT angiotensinogen
942 CD86 CD86 molecule
1636 ACE angiotensin I converting enzyme
3117 HLA-DQA1 major histocompatibility complex, class II, DQ alpha 1
3557 IL1RN interleukin 1 receptor antagonist
4210 MEFV MEFV innate immunity regulator, pyrin
5444 PON1 paraoxonase 1
6347 CCL2 C-C motif chemokine ligand 2

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Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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