Defective EXT1 causes exostoses 1, TRPS2 and CHDS
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- AGRIN
- AGRN
- EXT1
- EXT2
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HSPG1
- HSPG2
- KIAA0468
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
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Defective EXT2 causes exostoses 2
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- AGRIN
- AGRN
- EXT1
- EXT2
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HSPG1
- HSPG2
- KIAA0468
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
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Non-integrin membrane-ECM interactions
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- AGRIN
- AGRN
- CAK
- DAG1
- DDR1
- DDR2
- DMD
- EDDR1
- FGF2
- FGFB
- HSPG2
- KIAA0533
- KIAA0578
- KIAA1907
- LAMA
- LAMA1
- LAMA2
- LAMA3
- LAMA4
- LAMA5
- LAMB1
- LAMB2
- LAMB2T
- LAMB3
- LAMC1
- LAMC2
- LAMC3
- LAMM
- LAMNA
- LAMNB1
- LAMNB2
- LAMS
- NEP
- NRXN1
- NTN4
- NTRK4
- NTRKR3
- PALB
- PDGF1
- PDGF2
- PDGFA
- PDGFB
- PTK3A
- RTK6
- SIS
- TKT
- TRKE
- TTR
- TYRO10
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Respiratory syncytial virus (RSV) attachment and entry
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- AGRIN
- AGRN
- CD14
- CMKBRL1
- CX3CR1
- EGFR
- ERBB
- ERBB1
- ESOP1
- F
- FUR
- FURIN
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- GPR13
- HER1
- HSPG1
- HSPG2
- IGF1R
- KIAA0468
- L
- LY96
- M
- M2-1
- MD2
- N
- NCL
- OCI5
- P
- PACE
- PCSK3
- RAB5
- RAB5A
- RAB5B
- RAB5C
- RABL
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- TLR4
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Defective B3GAT3 causes JDSSDHD
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- AGRIN
- AGRN
- B3GAT3
- BCAN
- BEHAB
- BGN
- CALEB
- CSPG2
- CSPG3
- CSPG4
- CSPG5
- CSPG7
- DCN
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HSPG1
- HSPG2
- KIAA0468
- MCSP
- NCAN
- NEUR
- NGC
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SLRR1A
- SLRR1B
- VCAN
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HS-GAG biosynthesis
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- 3OST
- 3OST1
- 3OST2
- 3OST3A1
- 3OST3B1
- 3OST4
- 3OST5
- AGRIN
- AGRN
- EXT1
- EXT2
- GLCE
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HFRC
- HS2ST
- HS2ST1
- HS3OST5
- HS3ST1
- HS3ST2
- HS3ST3A
- HS3ST3A1
- HS3ST3B
- HS3ST3B1
- HS3ST4
- HS3ST5
- HS3ST6
- HS6ST
- HS6ST1
- HS6ST2
- HS6ST3
- HSPG1
- HSPG2
- HSST
- HSST1
- HSST2
- HSST3
- HSST4
- KIAA0448
- KIAA0468
- KIAA0836
- NDST1
- NDST2
- NDST3
- NDST4
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SLC35D2
- UGTREL8
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Defective B4GALT7 causes EDS, progeroid type
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- AGRIN
- AGRN
- B4GALT7
- BCAN
- BEHAB
- BGN
- CALEB
- CSPG2
- CSPG3
- CSPG4
- CSPG5
- CSPG7
- DCN
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HSPG1
- HSPG2
- KIAA0468
- MCSP
- NCAN
- NEUR
- NGC
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SLRR1A
- SLRR1B
- VCAN
- XGALT1
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Defective B3GALT6 causes EDSP2 and SEMDJL1
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- AGRIN
- AGRN
- B3GALT6
- BCAN
- BEHAB
- BGN
- CALEB
- CSPG2
- CSPG3
- CSPG4
- CSPG5
- CSPG7
- DCN
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HSPG1
- HSPG2
- KIAA0468
- MCSP
- NCAN
- NEUR
- NGC
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SLRR1A
- SLRR1B
- VCAN
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A tetrasaccharide linker sequence is required for GAG synthesis
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- AGRIN
- AGRN
- B3GALT6
- B3GAT1
- B3GAT2
- B3GAT3
- B4GALT7
- BCAN
- BEHAB
- BGN
- CALEB
- CSPG2
- CSPG3
- CSPG4
- CSPG5
- CSPG7
- DCN
- GLCATP
- GLCATS
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HSPG1
- HSPG2
- KIAA0468
- KIAA1963
- MCSP
- NCAN
- NEUR
- NGC
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SLRR1A
- SLRR1B
- VCAN
- XGALT1
- XT1
- XT2
- XYLT1
- XYLT2
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Integrin cell surface interactions
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- AGRIN
- AGRN
- BNSP
- BSG
- C21orf43
- CD11A
- CD11B
- CD11C
- CD18
- CD44
- CD47
- CD49B
- CD49D
- CDH1
- CDHE
- COL13A1
- COL16A1
- COL18A1
- COL23A1
- COL4A1
- COL4A2
- COL4A3
- COL4A4
- COL9A1
- COL9A2
- COL9A3
- COMP
- CR3A
- F11R
- FBN
- FBN1
- FGA
- FGB
- FGG
- FLK1
- FN
- FN1
- FNRA
- FNRB
- GP2B
- GP3A
- HSPG2
- HXB
- IBSP
- ICAM1
- ICAM2
- ICAM3
- ICAM4
- ICAM5
- ITGA1
- ITGA10
- ITGA11
- ITGA2
- ITGA2B
- ITGA3
- ITGA4
- ITGA5
- ITGA6
- ITGA7
- ITGA8
- ITGA9
- ITGAB
- ITGAD
- ITGAE
- ITGAL
- ITGAM
- ITGAV
- ITGAX
- ITGB1
- ITGB2
- ITGB3
- ITGB5
- ITGB6
- ITGB7
- ITGB8
- JAM1
- JAM2
- JAM3
- JCAM
- KDR
- LDC
- LHR
- LUM
- LW
- MDF2
- MDU2
- MDU3
- MER6
- MFI7
- MIC4
- MSK12
- MSK18
- MSK8
- OPN
- PECAM1
- SLRR2D
- SPP1
- THBS1
- TLCN
- TLN
- TNC
- TSP
- TSP1
- UVO
- VCAM1
- VEGFR2
- VEJAM
- VNRA
- VTN
- VTNR
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Attachment and Entry
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- 3a
- 7a
- ACE2
- AGRIN
- AGRN
- CTSL
- CTSL1
- E
- FUR
- FURIN
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- HAVCR1
- HEL-220
- HEL-S-70
- HSPG1
- HSPG2
- KIAA0468
- KIM1
- M
- N
- NRP
- NRP1
- OCI5
- PACE
- PCSK3
- PRSS10
- S
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- TIM1
- TIMD1
- TMPRSS2
- VCP
- VEGF165R
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HS-GAG degradation
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- AGRIN
- AGRN
- ELNR1
- GLB1
- GLB1L
- GLB1L2
- GLB1L3
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- GUSB
- HEP
- HPA
- HPA1
- HPA2
- HPR1
- HPSE
- HPSE1
- HPSE2
- HSE1
- HSPG1
- HSPG2
- HSS
- IDS
- IDUA
- KIAA0468
- NAGLU
- OCI5
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SGSH
- SIDS
- UFHSD1
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NCAM1 interactions
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- AGRIN
- AGRN
- ALTPRP
- ARTN
- AXT
- CACH1
- CACH2
- CACH3
- CACN1
- CACN2
- CACN4
- CACNA1C
- CACNA1D
- CACNA1G
- CACNA1H
- CACNA1I
- CACNA1S
- CACNB1
- CACNB2
- CACNB3
- CACNB4
- CACNL1A1
- CACNL1A2
- CACNL1A3
- CACNLB1
- CACNLB2
- CACNLB3
- CACNLB4
- CCHL1A1
- CCHL1A2
- CNTN2
- COL29A1
- COL4A1
- COL4A2
- COL4A3
- COL4A4
- COL4A5
- COL6A1
- COL6A2
- COL6A3
- COL6A5
- COL6A6
- COL9A1
- COL9A2
- COL9A3
- CSPG3
- EVN
- GDNF
- GDNFRA
- GDNFRB
- GFRA1
- GFRA2
- GFRA4
- KIAA1120
- KIAA1123
- MYSB
- NCAM
- NCAM1
- NCAN
- NEUR
- NRTN
- PRIP
- PRNP
- PRP
- PSPN
- PST
- PST1
- RETL1
- RETL2
- SIAT8B
- SIAT8D
- ST8SIA2
- ST8SIA4
- STX
- TAG1
- TAX1
- TRNR1
- TRNR2
- VWA4
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Retinoid metabolism and transport
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- A2MR
- AGRIN
- AGRN
- AKR1B10
- AKR1B11
- AKR1C1
- AKR1C3
- AKR1C4
- APC2
- APOA1
- APOA2
- APOA4
- APOB
- APOC2
- APOC3
- APOE
- APOER2
- APOM
- APR
- ARSDR1
- BCDO
- BCDO1
- BCDO2
- BCMO1
- BCO1
- BCO2
- CHDR
- CLPS
- CRBP1
- CRBP2
- DDH
- DDH1
- G3A
- GPC1
- GPC2
- GPC3
- GPC4
- GPC5
- GPC6
- GPIHBP1
- HBP1
- HSD17B5
- HSPG1
- HSPG2
- KIAA0119
- KIAA0468
- LDLR
- LIPD
- LPL
- LRAT
- LRP1
- LRP10
- LRP12
- LRP2
- LRP8
- NG20
- OCI5
- PALB
- PGFS
- PLB
- PLB1
- PNLIP
- PPSIG
- PSDR1
- RBP1
- RBP2
- RBP4
- RDH11
- RETSAT
- SDC
- SDC1
- SDC2
- SDC3
- SDC4
- SDR7C1
- ST7
- TTR
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Defective CHST6 causes MCDC1
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- ACAN
- AGC1
- CHST6
- CSPG1
- FM
- FMOD
- KERA
- LDC
- LUM
- MSK16
- OGN
- OIF
- OMD
- PRELP
- SLRR2A
- SLRR2B
- SLRR2C
- SLRR2D
- SLRR2E
- SLRR3A
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Defective ST3GAL3 causes MCT12 and EIEE15
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- ACAN
- AGC1
- CSPG1
- FM
- FMOD
- KERA
- LDC
- LUM
- MSK16
- OGN
- OIF
- OMD
- PRELP
- SIAT6
- SLRR2A
- SLRR2B
- SLRR2C
- SLRR2D
- SLRR2E
- SLRR3A
- ST3GAL3
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Keratan sulfate degradation
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- ACAN
- AGC1
- CSPG1
- ELNR1
- FM
- FMOD
- GLB1
- GLB1L
- GLB1L2
- GLB1L3
- GNS
- HEXA
- HEXB
- KERA
- LDC
- LUM
- MSK16
- OGN
- OIF
- OMD
- PRELP
- SLRR2A
- SLRR2B
- SLRR2C
- SLRR2D
- SLRR2E
- SLRR3A
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Defective B4GALT1 causes B4GALT1-CDG (CDG-2d)
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- ACAN
- AGC1
- B4GALT1
- CSPG1
- FM
- FMOD
- GGTB2
- KERA
- LDC
- LUM
- MSK16
- OGN
- OIF
- OMD
- PRELP
- SLRR2A
- SLRR2B
- SLRR2C
- SLRR2D
- SLRR2E
- SLRR3A
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Keratan sulfate biosynthesis
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- Aggrecan core protein
- Beta-1,4-galactosyltransferase 1
- Beta-1,4-galactosyltransferase 2
- Beta-1,4-galactosyltransferase 3
- Beta-1,4-galactosyltransferase 4
- Beta-1,4-galactosyltransferase 5
- Beta-1,4-galactosyltransferase 6
- Beta-1,4-glucuronyltransferase 1
- CMP-N-acetylneuraminate-beta-1,4-galactoside alpha-2,3-sialyltransferase
- CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,3-sialyltransferase 1
- CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,3-sialyltransferase 2
- CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,3-sialyltransferase 4
- Carbohydrate sulfotransferase 1
- Carbohydrate sulfotransferase 2
- Carbohydrate sulfotransferase 5
- Carbohydrate sulfotransferase 6
- Fibromodulin
- Keratocan
- Lumican
- Mimecan
- N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase 2
- N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase 3
- N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase 4
- Nucleotide sugar transporter SLC35D2
- Osteomodulin
- Prolargin
- Type 2 lactosamine alpha-2,3-sialyltransferase
- UDP-GlcNAc
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- ACAN
- AGC1
- B3GALT7
- B3GALT8
- B3GNT1
- B3GNT2
- B3GNT3
- B3GNT4
- B3GNT6
- B3GNT7
- B4GALT1
- B4GALT2
- B4GALT3
- B4GALT4
- B4GALT5
- B4GALT6
- B4GAT1
- CGS23
- CHST1
- CHST2
- CHST5
- CHST6
- CSPG1
- FM
- FMOD
- GGTB2
- GN6ST
- HFRC
- KERA
- LDC
- LUM
- MSK16
- NANTA3
- OGN
- OIF
- OMD
- PRELP
- SIAT10
- SIAT4
- SIAT4A
- SIAT4B
- SIAT4C
- SIAT6
- SLC35D2
- SLRR2A
- SLRR2B
- SLRR2C
- SLRR2D
- SLRR2E
- SLRR3A
- ST3GAL1
- ST3GAL2
- ST3GAL3
- ST3GAL4
- ST3GAL6
- STZ
- TMEM3
- UGTREL8
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ECM proteoglycans
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- ACAN
- AGC1
- AGRIN
- AGRN
- ASPN
- BCAN
- BEHAB
- BGN
- BNSP
- CD11C
- CD49B
- CMP
- COL9A1
- COL9A2
- COL9A3
- COMP
- CRTL1
- CRTM
- CSPG1
- CSPG2
- CSPG3
- CSPG7
- DAG1
- DCN
- DMP1
- DSPP
- FM
- FMOD
- FNRB
- GP2B
- GP3A
- HAPLN1
- HSPG2
- HXB
- HXBL
- IBSP
- ITGA2
- ITGA2B
- ITGA7
- ITGA8
- ITGA9
- ITGAB
- ITGAV
- ITGAX
- ITGB1
- ITGB3
- ITGB5
- ITGB6
- KIAA0533
- KIAA0816
- KIAA1907
- LAMA
- LAMA1
- LAMA2
- LAMA3
- LAMA4
- LAMA5
- LAMB1
- LAMB2
- LAMC1
- LAMM
- LAMNA
- LAMS
- LDC
- LRP10
- LRP4
- LUM
- MATN1
- MATN3
- MATN4
- MDF2
- MEGF7
- MSK12
- MSK16
- MSK8
- MUSK
- NCAM
- NCAM1
- NCAN
- NEUR
- ON
- PAI1
- PLANH1
- PLAP1
- PTPRS
- SERPINE1
- SLRR1A
- SLRR1B
- SLRR1C
- SLRR2D
- SLRR2E
- SPARC
- TGFB
- TGFB1
- TGFB2
- TGFB3
- TNC
- TNN
- TNR
- TNW
- TNX
- TNXB
- TNXB1
- TNXB2
- VCAN
- VNRA
- VTN
- VTNR
- XB
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Aflatoxin activation and detoxification
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- ACY1
- ACY3
- AFAR
- AFAR1
- AFAR2
- AFAR3
- AKR7
- AKR7A2
- AKR7A3
- AKR7A4
- AKR7L
- ASPA2
- CYP1A2
- CYP2A13
- CYP3A3
- CYP3A4
- CYP3A5
- DPEP1
- DPEP2
- DPEP3
- GGT
- GGT1
- GGT3
- GGT3P
- GGT5
- GGT6
- GGT7
- GGTL3
- GGTL5
- GGTLA1
- GST12
- GST2
- MDP
- MGST
- MGST1
- MGST2
- MGST3
- RDP
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Advanced glycosylation endproduct receptor signaling
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- A4
- AD1
- AGER
- APP
- CAPZA1
- CAPZA2
- DDOST
- ERK1
- ERK2
- G19P1
- HMG1
- HMGB1
- KIAA0115
- LGALS3
- MAC2
- MAPK1
- MAPK3
- OST48
- PRKCSH
- PRKM1
- PRKM2
- PRKM3
- RAGE
- S100A12
- S100B
- SAA1
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TRAF6 mediated NF-kB activation
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- A4
- AD1
- AGER
- APP
- CHUK
- DDX58
- EFP
- FIP3
- HMG1
- HMGB1
- IFIH1
- IKBA
- IKBB
- IKBKB
- IKBKG
- IKKA
- IKKB
- IPS1
- KBRAS1
- KBRAS2
- KIAA1271
- LYT10
- MAD3
- MAP3K1
- MAPKKK1
- MAVS
- MDA5
- MEKK
- MEKK1
- NEMO
- NFKB1
- NFKB2
- NFKB3
- NFKBI
- NFKBIA
- NFKBIB
- NKIRAS1
- NKIRAS2
- RAGE
- RELA
- RH116
- RIGI
- RNF135
- RNF147
- RNF85
- RNF87
- S100A12
- S100B
- SAA1
- TCF16
- TRAF2
- TRAF6
- TRAP3
- TRIM25
- TRIM4
- TRIP9
- VISA
- ZNF147
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TAK1-dependent IKK and NF-kappa-B activation
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- A4
- AD1
- AGER
- ALPK1
- APP
- BLU
- CARD15
- CARD4
- CARDIAK
- CHUK
- CROC1
- FIP3
- HMG1
- HMGB1
- IKBA
- IKBB
- IKBKB
- IKBKG
- IKKA
- IKKB
- IRAK
- IRAK1
- IRAK2
- ISG43
- KBRAS1
- KBRAS2
- KIAA0733
- KIAA1527
- LAK
- LYT10
- MAD3
- MAP3K7
- MAP3K7IP1
- MAP3K7IP2
- MAP3K7IP3
- N
- NEMO
- NFKB1
- NFKB2
- NFKB3
- NFKBI
- NFKBIA
- NFKBIB
- NKIRAS1
- NKIRAS2
- NOD1
- NOD2
- RAGE
- RELA
- RICK
- RIP2
- RIPK2
- RNF85
- RPS27A
- S100A12
- S100B
- SAA1
- T2BP
- TAB1
- TAB2
- TAB3
- TAK1
- TCF16
- TIFA
- TRAF6
- TRIP9
- UBA52
- UBA80
- UBB
- UBC
- UBCEP1
- UBCEP2
- UBE2N
- UBE2V
- UBE2V1
- UEV1
- USP18
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Electron transport from NADPH to Ferredoxin
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- ADX
- ADXR
- FDX1
- FDX1L
- FDX2
- FDXR
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